| CASE REPORT |
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| Year : 2016 | Volume
: 17
| Issue : 4 | Page : 142-145 |
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Uhl's anomaly: A rare case of portal hypertension
Rakesh Agarwal, Rajarshi Datta, Manjari Saha, Nirmalendu Sarkar
Department of General Medicine, IPGMER and SSKM Hospital, Kolkata, West Bengal, India
Correspondence Address:
Dr. Rakesh Agarwal
IPGMER and SSKM Hospital, Kolkata, West Bengal
India
 Source of Support: None, Conflict of Interest: None  | Check |
DOI: 10.4103/1995-705X.201779
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Uhl's anomaly is a rare congenital heart disease characterized by partial or complete absence of the right ventricular myocardium and high early mortality rates. We describe a case of Uhl's anomaly in a 27-year-old young male patient presenting with portal hypertension and esophageal varices. In this article, we review the literature associated with this condition and highlight a rare presentation of a rare disease. This report adds to our current knowledge of this exceedingly rare disorder. |
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